hamman rich syndrome

Acute interstitial pneumonitis was first described in 1935 by Louis Hamman and Arnold Rich and given the name HammanRich syndrome. Acute interstitial pneumonia AIP is a rare and fulminant form of diffuse lung injury originally described by Hamman and Rich in 1935 12.

Acute Interstitial Pneumonitis Radiology Reference Article Radiopaedia Org

An acute to chronic inflammatory process of the lungs the healing stage of diffuse alveolar damage or acute interstitial pneumonia either idiopathic or associated with collagen-vascular diseases.

. Acute interstitial pneumonia also known as Hamman-Rich Syndrome is a rare and severe form of idiopathic interstitial lung disease 1 originally described by Hamman and Rich in 1935. Hamman-Rich syndrome is a rapidly progressive interstitial lung disease with acute respiratory distress syndrome physiology. Subacute form also called Hamman-Rich syndrome qv. It is considered the only acute process among the idiopathic interstitial pneumonias.

Hamman-rich Syndrome refers to an acute and rapidly progressing pulmonary disease. Acute interstitial pneumonitis AIP also known as Hamman-Rich syndrome is a rapidly progressive non-infectious interstitial lung disease of unknown etiology. It is often distinguished from other similar pulmonary pathologies based on the clinical course laboratory findings bronchoalveolar lavage testing and pathology report. Hammans syndrome also known as Macklins syndrome is a syndrome of spontaneous subcutaneous emphysema and pneumomediastinum sometimes associated with pain and less commonly dyspnea dysphonia and a low-grade fever.

1 Acute onset of respiratory failure similar to ARDS 2 Bilateral lung infiltrates on radiographs 3. It carries a grave prognosis and a high early mortality rate. AIP is classified as an idiopathic interstitial pneumonia IIP and among the IIPs it has the most acute onset and rapidly progressive course 1-4. During the 1935 year Louis Hamman and Arnold Rich explained it for the first time and called it meteoric interstitial fibrosis associated with the lungs.

AIP is similar in presentation to the acute respiratory distress. An acute to chronic inflammatory process of the lungs the healing stage of diffuse alveolar damage or acute interstitial pneumonia either idiopathic or associated with collagen-vascular diseases. And in whose lungs pathologic studies revealed a diffuse interstitial fibrosis involving the interalveolar septa in particular. In 1935 Hamman and Rich 1 of Johns Hopkins first described a syndrome which they had observed in three patients characterized by a gradual onset of cough dyspnea and cyanosis.

Subacute form also called Hamman-Rich syndrome qv. This disease is characterised by the following criteria 2. Hammans syndrome can cause Hammans sign an unusual combination of sounds that can be heard with a stethoscope.